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中华移植杂志(电子版) ›› 2021, Vol. 15 ›› Issue (03) : 172 -174. doi: 10.3877/cma.j.issn.1674-3903.2021.03.010

所属专题: 经典病例

病例报告

Kartagener综合征行双肺移植伴双侧膈神经损伤一例
郑媛媛1, 孙燕燕1, 施科达1, 泮辉1, 李洲斌1, 朱曼华1, 韩威力1,()   
  1. 1. 310003 杭州,浙江大学医学院附属第一医院肺移植科
  • 收稿日期:2020-11-24 出版日期:2021-06-25
  • 通信作者: 韩威力

Double lung transplantation in a Kartagener syndrome patient suffering from bilateral phrenic nerve injury

Yuanyuan Zheng1, Yanyan Sun1, Keda Shi1, Hui Pan1, Zhoubin Li1, Manhua Zhu1, Weili Han1,()   

  1. 1. Department of Lung Transplantation, the First Affiliated Hospital, Zhejiang University School of Medicine, Hangzhou 310003, China
  • Received:2020-11-24 Published:2021-06-25
  • Corresponding author: Weili Han
引用本文:

郑媛媛, 孙燕燕, 施科达, 泮辉, 李洲斌, 朱曼华, 韩威力. Kartagener综合征行双肺移植伴双侧膈神经损伤一例[J]. 中华移植杂志(电子版), 2021, 15(03): 172-174.

Yuanyuan Zheng, Yanyan Sun, Keda Shi, Hui Pan, Zhoubin Li, Manhua Zhu, Weili Han. Double lung transplantation in a Kartagener syndrome patient suffering from bilateral phrenic nerve injury[J]. Chinese Journal of Transplantation(Electronic Edition), 2021, 15(03): 172-174.

图1 Kartagener综合征患者肺移植术前胸部CT影像
图2 Kartagener综合征患者肺移植术中行右侧移植肺减容术
图3 Kartagener综合征患者肺移植术后3个月肺部CT示无明显感染及排斥反应表现
1
Knowles MR, Daniels LA, Davis SD, et al. Primary ciliary dyskinesia. Recent advances in diagnostics, genetics, and characterization of clinical disease[J]. Am J Resp Crit Care, 2013188(8): 913-922.
2
Yazicioglu A, Alici IO, Karaoglanoglu N, et al. Pitfalls and challenges of lung transplant in a patient with Kartagener syndrome and scoliosis[J].Exp Clin Transplan, 2018, 16(2): 237-241.
3
毛文君,陈静瑜,郑明峰,等. 双肺移植治疗Kartagener综合征一例[J/CD]. 中华胸部外科电子杂志2014, 1(1): 66-68.
4
Hayes D Jr, Reynolds SD, Tumin D. Outcomes of lung transplantation for primary ciliary dyskinesia and Kartagener syndrome[J]. J Heart LungTranspl, 2016, 35(11): 1377-1378.
5
Engesaeth VG, Warner JO, Bush A. New associations of primary ciliary dyskinesia syndrome[J]. Pediatr Pulmonol, 1993, 16(1): 9-12.
6
Brioude G, D′journo XB, Reynaud-Gaubert M, et al. Bronchial fistula after lobar size reduction for bilateral lung transplantation in Kartagener′s syndrome: a surgical challenge[J]. Interact Cardiov Thorac Surg, 2013, 17(1): 184-186.
7
Kayawake H, Chen-Yoshikawa TF, Aoyama A, et al. Surgical management of bronchial stumps in lobar lung transplantation[J]. J Thorac Cardiovasc Surg, 2018, 156(1): 451-460.
8
Mentzer SJ, Aranki SF, Reilly JJ, et al. Single-lung transplantation in situs inversus[J]. Ann Thorac Surg, 1994, 58(4):1176-1178.
9
Sano Y, Oto T, Toyooka S, et al. Phrenic nerve paralysis following lung transplantation[J]. Kyobu Geka, 2007, 60(11): 993-997.
10
Freeman RK, Wozniak TC, Fitzgerald EB. Functional and physiologic results of video-assisted thoracoscopic diaphragm plication in adult patients with unilateral diaphragm paralysis[J]. Ann Thorac Surg, 2006, 81(5): 1853-1857.
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