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中华移植杂志(电子版) ›› 2021, Vol. 15 ›› Issue (03) : 161 -165. doi: 10.3877/cma.j.issn.1674-3903.2021.03.007

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I型酪氨酸血症患儿活体肝移植围手术期麻醉管理
杨文鹤1, 张梁1,(), 薛富善1, 朱志军2   
  1. 1. 100050 北京,首都医科大学附属北京友谊医院麻醉科
    2. 100050 北京,首都医科大学附属北京友谊医院普外科;100050 北京,国家消化系统疾病临床医学研究中心肝移植分中心;100050 北京,首都医科大学儿童肝脏移植临床诊疗与研究中心
  • 收稿日期:2021-04-07 出版日期:2021-06-25
  • 通信作者: 张梁
  • 基金资助:
    首都医科大学附属北京友谊医院科研启动基金(YYQDKT2018-12)

Anesthetic management of pediatric patients with hereditary tyrosinemia type 1 undergoing living-donor liver transplantation

Wenhe Yang1, Liang Zhang1,(), Fushan Xue1, Zhijun Zhu2   

  1. 1. Department of Anesthesiology, Beijing Friendship Hospital, Capital Medical University, Beijing 100050, China
    2. Department of General Surgery, Beijing Friendship Hospital, Capital Medical University, Beijing 100050, China; Liver Transplantation Center, National Clinical Research Center for Digestive Diseases, Beijing 100050, China; Clinical Center for Pediatric Liver Transplantation, Capital Medical University, Beijing 100050, China
  • Received:2021-04-07 Published:2021-06-25
  • Corresponding author: Liang Zhang
引用本文:

杨文鹤, 张梁, 薛富善, 朱志军. I型酪氨酸血症患儿活体肝移植围手术期麻醉管理[J/OL]. 中华移植杂志(电子版), 2021, 15(03): 161-165.

Wenhe Yang, Liang Zhang, Fushan Xue, Zhijun Zhu. Anesthetic management of pediatric patients with hereditary tyrosinemia type 1 undergoing living-donor liver transplantation[J/OL]. Chinese Journal of Transplantation(Electronic Edition), 2021, 15(03): 161-165.

表1 接受活体肝移植的HT-1患儿和供肝基本资料
表2 HT-1患儿肝移植术中、术后情况及HAZ评分结果
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